Pre- and postnatal imaging of Pai syndrome with spontaneous intrauterine closure of a frontal cephalocele.

Pai syndrome is a rare congenital disorder characterized by cutaneous polyps of the face, pericallosal lipoma and median cleft lip. We report on a newborn girl with a variant of Pai syndrome presenting with all typical findings except a median cleft. In addition, fetal sonography and MRI showed the unique intrauterine evolution of a cephalocele into an atretic cephalocele.

Maḥzor mi-kol ha-shanah : ke-minhag Ashkenaz u-Polin ṿe-ʿal pi rov kaṿanot ha-paiṭan neḥleḳu le-shenayim ṿe-arbaʿ ḥalaḳim ṿe-etsel kol ḥelek ve-ḥelek tefilat shaḥariti

Bd. 1, Rosh ha-shanah, Shabat Shuvah