Temper outbursts in Prader-Willi syndrome: causes, behavioural and emotional sequence and responses by carers

Background: Temper outbursts are common in Prader-Willi syndrome but rarely described in detail. This study investigated the phenomenology of temper outbursts in terms of antecedents, sequence of behaviours and emotions and intervention strategies used.

Method: A semi-structured interview about temper outbursts was conducted with the main carers of seven children (9.5 to 16.7 years) and seven adults (24.7 to 47.10 years) with Prader-Willi syndrome (10 male, 4 female). Reliability and validity of the interview results was established.

Results: Various setting events increased and reduced the likelihood of temper outbursts. The most common antecedent was a change to routine or expectation. There were marked similarities in the sequence of behaviours and emotions during temper outbursts, with anger rising quickly followed by expressions of remorse and distress at the end of an outburst.

Discussion: The sequence of behaviours and emotions within outbursts was similar to that described in temper tantrums in typical development. Cognitive and emotional processes are likely to be important in the understanding of temper outbursts with implications for early intervention.

'Easter Rising', 1914-1918-online. International Encyclopedia of the First World War

Although a military failure, the 1916 rebellion transformed Ireland by destroying the possibility of a political settlement between Irish nationalists and the British state and by popularising a republican movement prepared to use violence to achieve independence. This essay surveys the political background to the Easter Rising, its planning, the motivations and ideology of the rebels and the battle for Dublin. It concludes by assessing the Rising’s political impact and briefly summarising historiographical interpretations and commemorative trends. It argues that the origins, conduct, impact and aftermath of the insurrection are best understood within the wider context of the First World War.

Islamist Versus Islamist: Rising Challenge in Gaza

Islam's diversity is a direct result of centuries of schism and factionalism, and presents a challenge to the original spirit of unity as envisaged by its founder, the Prophet Mohammed. Rivalry within Islam undermines the precedent notion of unity through communal belonging (tawhid and ummah). Yet in the twenty-first century this diversity is ignored, and political Islam is represented as being more of a monolith than a spectrum of ideas and aspirations. Generally, the materialization of new Islamist groups is a challenge to those who hold that unity is all. In the Gaza Strip, specifically, the dominant Islamist actor, Hamas, is facing internal challenges from other Islamist elements. These rival Islamists are also influenced by events across their border in post-revolutionary Egypt where a plethora of new Islamist actors are vying for political space and power. This article deals with Hamas's Islamist rivals, and the effects they have had on Hamas's governance of the Gaza Strip, and political and religious legitimacy within it. It will focus on ideological and violent disputes between the Islamist elements in Gaza, and the means by which Hamas and its security elements have tackled newly emerging rivals.

The political legacy of World war I and the Easter Rising in Longford

During the Irish War of Independence, between 1919 and 1921, Longford was one of the centres of the Irish Republican Army's guerrilla campaign against British rule in Ireland. The county's emergence as a centre of republican activity appears incongruous in light of its relatively peaceful history up to that point and in view of the fact that, outside of Dublin, its neighbouring Leinster counties were not particularly strongholds of IRA resistance. The explanation for Longford's role during the crucial years of the independence campaign is to be found in the political ransformation that occurred in the county in the crucial period of turmoil encompassing World War I and the Easter Rising.

The first month of evolution of the slow-rising Type IIP SN 2013ej in M74

We present early photometric and spectroscopic observations of SN 2013ej, a bright Type IIP supernova (SN) in M74. SN 2013ej is one of the closest SNe ever discovered. The available archive images and the early discovery help to constrain the nature of its progenitor. The earliest detection of this explosion was on 2013 July 24.125 UT and our spectroscopic monitoring with the FLOYDS spectrographs began on July 27.7 UT, continuing almost daily for two weeks. Daily optical photometric monitoringwas achieved with the 1mtelescopes of the Las Cumbres Observatory Global Telescope (LCOGT) network, and was complemented by UV data from Swift and near-infrared spectra from Public ESO Spectroscopic Survey of Transient Objects and Infrared Telescope Facility. The data from our monitoring campaign show that SN 2013ej experienced a 10 d rise before entering into a well-defined plateau phase. This unusually long rise time for a Type IIP has been seen previously in SN 2006bp and SN 2009bw. A relatively rare strong absorption blueward of Hα is present since our earliest spectrum. We identify this feature as Si II, rather than high-velocity Hα as sometimes reported in the literature. 

The Rising (Centenary Edition) Ireland: Easter 1916

The Easter Rising of 1916 not only destroyed much of the centre of Dublin - it changed the course of Irish history. But why did it happen? What was the role of ordinary people in this extraordinary event? What motivated them and what were their aims? These basic questions continue to divide historians of modern Ireland.

The Rising is the story of Easter 1916 from the perspective of those who made it, focusing on the experiences of rank and file revolutionaries. Fearghal McGarry makes use of a unique source that has only recently seen the light of day - a collection of over 1,700 eye-witness statements detailing the political activities of members of Sinn Féin and militant groups such as the Irish Republican Brotherhood. This collection represents one of the richest and most comprehensive oral history archives devoted to any modern revolution, providing new insights on almost every aspect of this seminal period.

The Rising shows how people from ordinary backgrounds became politicized and involved in the struggle for Irish independence. McGarry illuminates their motives, concerns, and aspirations, highlighting the importance of the Great War as a catalyst for the uprising. He concludes by exploring the Rising's revolutionary aftermath, which in time saw the creation of the independent state we see today.

Published to mark the centenary of the Easter Rising, this edition includes a new preface which reflects on the continuing importance of the Easter Rising as a symbol of Irish nationhood and which looks at the centenary commemorations in both Ireland and the UK within the wider context of the 'Decade of Centenaries.'

Remembering 1916: The Easter Rising, the Somme and the Politics of Memory in Ireland

The year 1916 witnessed two events that would profoundly shape both
politics and commemoration in Ireland over the course of the following
century. Although the Easter Rising and the Battle of the Somme were
important historical events in their own right, their significance also lay
in how they came to be understood as iconic moments in the emergence
of Northern Ireland and the Irish Republic. Adopting an interdisciplinary
approach drawing on history, politics, anthropology and cultural
studies, this volume explores how the memory of these two foundational
events has been constructed, mythologised and revised over the course
of the past century. The aim is not merely to understand how the Rising
and Somme came to exert a central place in how the past is viewed in
Ireland, but to explore wider questions about the relationship between
history, commemoration and memory.

A rising e-channel tide lifts all boats? the impact of manufacturer multi-channel encroachment on traditional selling and leasing

Organizing and managing channels of distribution is an important marketing task. Due to the emergence of electronic commerce on the Internet, e-channel distribution systems have been adopted by many manufacturers. However, academic and anecdotal evidence both point to the pressures arising from this new e-channel manufacturing environment. Questions marks therefore remain on how the addition of this e-channel affects the traditional marketing strategies of leasing and selling. We set up several two-period dual-channel models in which a manufacturer sells a durable product through both a manufacturer-owned e-channel and an independent reseller (leaser) who adopts selling (leasing) to consumers. Our main results indicate that, direct selling cost aside, product durability plays an important role in shaping the strategies of all members. With either marketing strategy, the additional expansion of an e-channel territory may secure Pareto gains, in which all members benefit.

Adaptable housing design for climate change adaptation

It is predicted that climate change will result in rising sea levels, more frequent and extreme weather events, hotter and drier summers and warmer and wetter winters. This will have a significant impact on the design of buildings, how they are kept cool and how they are weathered against more extreme climatic conditions. The residential sector is already a significant environmental burden with high associated operational energy. Climate change, and a growing population requiring residence, has the potential to exacerbate this problem seriously. New paradigms for residential building design are required to enable low-carbon dioxide operation to mitigate climate change. They must also face the reality of inevitable climate change and adopt climate change adaptation strategies to cope with future scenarios. However, any climate adaptation strategy for dwellings must also be cognisant of adapting occupant needs, influenced by ageing populations and new technologies. This paper presents concepts and priorities for changing how society designs residential buildings by designing for adaptation. A case study home is analysed in the context of its stated aims of low energy and adaptability. A post-occupancy evaluation of the house is presented, and future-proofing strategies are evaluated using climate projection data for future climate change scenarios.

1916-2016. The 1916 Easter Rising

Commissioned by An Post to commemorate the centenary of the Easter Rising, this illustrated book draws on eye-witness accounts to assess this key turning-point in modern Irish history. Leading historian Fearghal McGarry explores the impact of events at the General Post Office, as well as setting the rebellion in its wider historical context. His account concludes with an assessment of the Rising's commemoration since 1916 and a commentary on the definitive stamps issued by An Post to mark the formative event in the emergence of an independent Irish nation.

Letter, to Oliver Hawes Spencer, Cheraw, SC, 1824 March 25

This letter is from Henry D. to O. H. Spencer.

Letter, Wadesboro, NC, to Oliver Hawes Spencer, Cheraw, SC, 1811 January 15

This letter is to O. H. Spencer.

Letter, Cedar Hill, NC, to Oliver Hawes Spencer, Cheraw, SC, 1842 November 3

This letter is to O. H. Spencer.

Letter, Georgetown, SC, to Oliver Hawes Spencer, Chesterfield, SC, 1832 July 26

This letter is from E. Materman to O. H. Spencer.