Etude des causes du faible captage de naissain d'huitre creuse dans le Bassin d'Arcachon en 1998

Après une quinzaine d'années pendant lesquelles le captage de l'huître creuse a été normal ou pléthorique dans le Bassin d'Arcachon, la saison 1998 a donné de très faibles résultats. Plusieurs hypothèses ont été émises pour expliquer ce déficit : conditions climatiques et hydrologiques exceptionnelles, manque de nourriture pour les larves, maladie, contamination du milieu ayant eu un impact sur les larves ou sur leur nourriture. Chacune de ces hypothèses a été étudiée, en reprenant les données de 1998 lorsqu'elles étaient disponibles, et en acquérant l'ensemble des données nécessaires à l'explication du phénomène au cours de la saison de reproduction 1999.

A new species of Phylloicus Muller, 1880 (Trichoptera: Calamoceratidae), from southeastern Brazil, including descriptions of larval and pupal stages

The cosmopolitan family Calamoceratidae Ulmer, 1906, has 8 living genera, among them Phylloicus Muller, 1880, with species distributed from South to Central America. This genus is characterized by its dark-colored adults (brown to black) with diurnal to crepuscular habits. In this paper, the adults, pupae, and larvae of Phylloicus camargoi n. sp. are described and illustrated. The new species is easily diagnosed by male tergum X bearing a short, digitate, setose, basodorsal process; 2 short, digitate, hairless, lateral processes; and 2 pairs of very short processes on the posterior margin: a pair of digitate, hairless, posterolateral processes, and a pair of posteromesal processes. Additional diagnostic characters are the presence of 3 color bands on the forewings, 2 golden longitudinal bands and a white transversal one.

COEXISTENCE OF TWO CHRONIC NEUROPATHIES IN A YOUNG CHILD: CHARCOT-MARIE-TOOTH DISEASE TYPE 1A AND CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY

We report an 18-month-old Charcot-Marie-Tooth type 1A (CMT1A) patient who developed a rapid-onset neuropathy, with proximal and distal weakness, and non-uniform nerve conduction studies. The neuropathy responded well to immunomodulation, confirming the coexistence of an inherited and an inflammatory neuropathy. Unexpected clinical and/ or electrophysiological manifestations in CMT1A patients should alert clinicians to concomitant inflammatory neuropathy. In addition, this association raises reflections about disease mechanism in CMT1A. Muscle Nerve 42: 598-600, 2010

Compound Charcot-Marie-Tooth disease may determine unusual and milder phenotypes

Compound forms of Charcot-Marie-Tooth (CMT) disease have been recently associated with unusually severe neuropathies, an observation that prompted the proposition that the additive effects of two mutations should be searched in patients whose clinical severity falls outside the common CMT phenotypes. In this report, we present a father and a daughter with a very mild and unusual disease that segregates with two mutations in PMP22 gene, the 17p11.2-p12 duplication and a Ser72Leu point mutation. We propose that the deleterious effects of each mutation are partially compensated by the functional effect of the other.

Characterizing the phenotypic manifestations of MFN2 R104W mutation in Charcot-Marie-Tooth type 2

Mutations of the mitofusin 2 (MFN2) gene have been reported to be the most common cause of the axonal form of Charcot Marie Tooth disease (CMT). The aim of this study was to describe a de novo MFN2 p.R104W mutation and characterize the associated phenotype. We screened the entire coding region of MFN2 gene and characterized its clinical phenotype, nerve conduction studies and sural nerve biopsy. Neuropsychological tests and brain MRI were also performed. A de nova mutation was found in exon 4 (c.310C > T; p.R104W). In addition to a severe and early onset axonal neuropathy, the patient presented learning problems, obesity, glucose intolerance, leukoencephalopathy, brain atrophy and evidence of myelin involvement and mitochondrial structural changes on sural nerve biopsy. These results suggest that MFN2 p.R104W mutation is as a hot-spot for MFN2 gene associated to a large and complex range of phenotypes. (C) 2011 Elsevier B.V. All rights reserved.

Review of Voices from the shopfloor: Dramas of the employment relationship,/by Anne-Marie Greene. Aldershot : Ashgate, 2001

This research monograph seeks, as the author puts it, ‘to demonstrate the utility of ethnographic research methods to industrial relations in the developing world’. To this end, the author provides case studies of two lock factories in the West Midlands of England, with data sourced from interviews and observations by the author during a period of two decades in the case of one, and a rather shorter period in the case of the other. The insights gleaned from these two case studies are then considered in the light of the ethnographic literature on industrial relations in the developing world. The body of the book comprises three main chapters which successively examine the issues of paternalism, gender and family, and collective action in the two factories.

O campo da energia elétrica no Brasil de 1880 a 2002

Como a energia elétrica é um bem essencial em nossa sociedade, este artigo analisa a evolução da formação e estruturação do setor elétrico brasileiro, desde o surgimento da energia elétrica no Brasil, em 1880, até o final de 2002. A análise se faz a partir da descrição histórica linear, com cortes em fatos determinantes que são detalhados e analisados, mostrando-se os principais atores sociais, seus interesses e influência, na data desses cortes. Foi utilizada a metodologia qualitativa e o referencial da teoria institucional, com base na configuração do campo organizacional, além da análise de documentos e de entrevistas em profundidade, realizadas com dirigentes do setor que participaram dessa história. Finalmente, o artigo mostra como o ambiente externo é o principal elemento que influencia a trajetória do setor elétrico, nomeadamente quanto ao investimento ou não de recursos financeiros.