Atrichia, abnormal EEG, epilepsy and mental retardation in two sisters

Two daughters of a nonconsanguineous couple are described. Both present mental retardation, epileptic seizures, congenital atrichia, histologically anomalous skin and abnormal EEG pattern. From a discussion of the literature on atrichia, the forms without involvement of teeth, nails and hidrosis, among which recessive inheritance prevails, are distinguished from each other. None of them coincide with the syndrome described here.

Síndrome nefrótica primária grave em crianças: descrição clínica e dos padrões histológicos renais de seis casos

Os autores relatam os casos de seis crianças com síndrome nefrótica primária grave de padrão histológico renal incomum na rotina cotidiana dos nefrologistas e patologistas. O diagnóstico da doença foi realizado nas faixas etárias de 3 a 9 meses de idade (n = 4), aos 2 anos e 4 meses (n = 1) e aos 11 anos (n = 1). Um paciente foi prematuro, duas pacientes eram irmãs e seus pais eram primos de primeiro grau. Todos apresentavam edema generalizado; dois pacientes apresentavam desnutrição e hipotireoidismo e dois apresentavam hipertensão arterial e insuficiência renal. A histologia renal mostrou esclerose mesangial difusa (n = 3), proliferação mesangial (n = 2) e síndrome nefrótica do tipo finlandês (n = 1). Quatro pacientes faleceram, as causas de óbito foram infecção (n = 2), insuficiência renal (n = 1) e acidose metabólica (n = 1). Entre os sobreviventes, um paciente foi tratado com vitaminas, tiroxina, captopril e indometacina, apresentando aumento da albumina sérica e melhora do crescimento. O outro paciente apresentava insuficiência renal terminal, sendo tratado com diálise e transplante renal.

Phylogeography of the Solanaceae-infecting Basidiomycota fungus Rhizoctonia solani AG-3 based on sequence analysis of two nuclear DNA loci

Background: the soil fungus Rhizoctonia solani anastomosis group 3 (AG-3) is an important pathogen of cultivated plants in the family Solanaceae. Isolates of R. solani AG-3 are taxonomically related based on the composition of cellular fatty acids, phylogenetic analysis of nuclear ribosomal DNA (rDNA) and beta-tubulin gene sequences, and somatic hyphal interactions. Despite the close genetic relationship among isolates of R. solani AG-3, field populations from potato and tobacco exhibit comparative differences in their disease biology, dispersal ecology, host specialization, genetic diversity and population structure. However, little information is available on how field populations of R. solani AG-3 on potato and tobacco are shaped by population genetic processes. In this study, two field populations of R. solani AG-3 from potato in North Carolina (NC) and the Northern USA; and two field populations from tobacco in NC and Southern Brazil were examined using sequence analysis of two cloned regions of nuclear DNA (pP42F and pP89).Results: Populations of R. solani AG-3 from potato were genetically diverse with a high frequency of heterozygosity, while limited or no genetic diversity was observed within the highly homozygous tobacco populations from NC and Brazil. Except for one isolate (TBR24), all NC and Brazilian isolates from tobacco shared the same alleles. No alleles were shared between potato and tobacco populations of R. solani AG-3, indicating no gene flow between them. To infer historical events that influenced current geographical patterns observed for populations of R. solani AG-3 from potato, we performed an analysis of molecular variance (AMOVA) and a nested clade analysis (NCA). Population differentiation was detected for locus pP89 (Phi(ST) = 0.257, significant at P < 0.05) but not for locus pP42F (Phi(ST) = 0.034, not significant). Results based on NCA of the pP89 locus suggest that historical restricted gene flow is a plausible explanation for the geographical association of clades. Coalescent-based simulations of genealogical relationships between populations of R. solani AG-3 from potato and tobacco were used to estimate the amount and directionality of historical migration patterns in time, and the ages of mutations of populations. Low rates of historical movement of genes were observed between the potato and tobacco populations of R. solani AG-3.Conclusion: the two sisters populations of the basidiomycete fungus R. solani AG-3 from potato and tobacco represent two genetically distinct and historically divergent lineages that have probably evolved within the range of their particular related Solanaceae hosts as sympatric species.

HERITABILITY OF THE NUMBER OF OVARIOLES IN HONEY-BEE WORKERS (APIS-MELLIFERA L) (HYM, APIDAE)

Narrow and broad sense heritabilities (h(2)) of the number of ovarioles in Apis mellifera L. workers were estimated using two distinct data sets, based on groups of half (queens inseminated by several drones) and super-sisters (single drone insemination). The values found are in the usual range for economically important characters (0.25-0.38).

Heritability of the number of ovarioles in honey bee workers (Apis mellifera L.) (hym.:apidae)

Narrow and broad sense heritabilities (h2) of the number of ovarioles in Apis mellifera L. workers were estimated using two distinct data sets, based on groups of half (queens inseminated by several drones) and super-sisters (single drone insemination). The values found are in the usual range for economically important characters (0.25-0.38).

A frágil realidade de plástico: um estudo comparativo da imagem Casa de Bonecas em henrik ibsen e katherine mansfield

Considering the importance of significations in literary works, this paper proposes a comparative study of the image of the Doll's House in Henrik Ibsen's play ADoll's House (1879), and Katherine Mansfield's short story The Doll's House, published in the book The Dove's Nest (1923), based on the theories of Gaston Bachelard and Jean Baudrillard. In both cases, one notices that the presence of this image indicatesnot only the construction of these works' environment, but also a criticism of the bourgeois model of a perfect and flawless society, as the described image refers to. However, even though this image shares the same idea in both works, it will be explored differentlyin each case, whether through the search of Nora's character in escaping social conformity as in Ibsen, or through the subtle childlike game experienced by the Kelvey sisters, asin Mansfield.

Caso Rushdie: uma análise da relação entre islamismo e direitos humanos

Fundação de Amparo à Pesquisa do Estado de São Paulo (FAPESP)

A criança com psoríase e as relações vinculares com a mãe e a família

Coordenação de Aperfeiçoamento de Pessoal de Nível Superior (CAPES)

A política de ensino do exército brasileiro na Nova República: o projeto de modernização (1985-2000)

Coordenação de Aperfeiçoamento de Pessoal de Nível Superior (CAPES)

Famílias com gêmeos: um estudo sobre o relacionamento fraterno e a dinâmica das relações familiares

Pós-graduação em Psicologia do Desenvolvimento e Aprendizagem - FC

O reino Visigodo: catolicismo e permanências pagãs

What became accustomed to call “paganism” is undoubtedly one of the most significant forms of what is designated as “popular religiosity”. This expression, which seems useful when a generalization is required, shows all its weakness when a more precise and objective observation of a particular religion is attempted. Would the official visigothic kingdom’s “conversion” to Catholicism, with Recardo (586-601) at the Council of Toledo of 589 have effectively matched to the “conversion” of this kingdom’s population? Firstly, it is necessary to consider, in beyond the exalting intentions of the sources of that moment, that mass conversions do not imply a radical change in the convictions and religious practices of an entire people. Secondly, that “conversion” and “Christianization” are not synonymous. “Religiosity”, which includes the “conversion”, implies a fundamental religious attitude, which can simply be interior and personal. On the other hand, “religion”, in which “Christianization” is included, would correspond to a public aspect, institutionalized, which elaborates a set of techniques aiming, as in the case of “religiosity”, the guarantee of the supernatural Thus, elevated to the position of “official religion,” Catholic Christianity would live with a series of rites, rituals, devotions, from the previous “religiosity” that, through its ecclesiastical perspective, would be reprehensible, considered marginal and something that would lead to error. However, on the eve of the Muslim invasion in 711, not only among the laity but even in ecclesiastical segments, the manifestations of the “paganism” still were aim of coactive condemnation in the Catholic kingdom of Toledo’s councils.

Allonursing in river buffalo, Bubalus bubalis: Nepotism, incompetence, or thievery?

Allonursing was investigated in a dairy herd of 30 river buffalo cows and their calves. The primary behavioural variables were solicitations of allonursing by calves and acceptances of calves by cows. The sample of cows included a group of nine half-sisters, two additional pairs of half-sisters, and a pair of full-sisters. All of the calves were half-siblings owing to putative common paternity. Ancillary variables were age, milk-yield and docility of cows, as well as age, sex, weight and growth rate of calves. Three hundred and fifty-one instances of allonursing and 341 of filial nursing were recorded. There were large individual differences in the cows' tendencies to accept their own offspring and non-filial calves, and for the calves to successfully solicit milk from their mothers and other cows. Thirteen of the 30 cows accounted for 97% of the allonursing. Frequent allonursing was correlated with decreased growth rate in the donors' calves. Allonursing was unrelated to kinship or reciprocal relationships among the cows, and was associated with a lack of maternal experience in young cows and apparent milk theft by hungry calves whose mothers were not providing them with sufficient milk. © 1995 The Association for the Study of Animal Behaviour.

Indústria frigorífica halal no Brasil, mão-de-obra islamita e estado de exceção

In the last decade, Brazilian meat export rates for Muslim religious countries have increased, and also has the immigration of Africans workers able to perform the slaughter following the precepts of Islam - religion that has expanded in the world, and thus, has the halal food segment. Halal, the Islamic ideology, means lawful, authorized by God: are those products that Allah in the Holy Qur'an releases for human consumption. To get halal certification some measures during slaughter/processing food should be taken. In the case of the slaughterhouses the animal must be slaughtered by a Muslim. Consequently, the demand for this skilled labor makes many African-Muslims get jobs in factories owned by BRF Foods, JBS and Marfrig; refugees and with their citizenship rights committed, these individuals live in a socio-political state of exception and overexploitation. In this study we intend to discuss the object of study Islamist workforce in Brazilian halal meat industry using the theoretical reflections of Giorgio Agamben (Homo Sacer in 2002, and State of Exception, 2004) and David Harvey (The Condition of Postmodernity, 2008, and The New Imperialism, 2004) to address the situation of immigrants in the meat business in Brazil, specially those on the halal certification segment, whose working and living conditions were described from academic studies and primary sources (articles in newspapers / magazines, websites, immigration official data). In addition we use the works of Rogério Heasbaert (O mito da desterritorialização, 2007) and Robert Kurz (Os paradoxos dos direitos humanos: inclusão e exclusão na modernidade, 2003) to discuss human mobility in this new century