Dietoterapia en paciente con linfangiectasia intestinal primaria y ascitis quilosa de repetición.


Autoria(s): Campos Martín, C; Rabat Restrepo, JM; Sendón Pérez, A; Fernández-Argüelles García, A
Data(s)

07/02/2013

07/02/2013

01/11/2007

Resumo

OBJECTIVES Primary intestinal lymphangiectasia is a lymphatic system's disorder, where lymphatic drainage is blockaged. Clinically it produces malabsorption, protein-losing enteropathy, hypogammaglobulin in blood, and several degrees of malnutrition. Its treatment is not easy and includes dietetic-therapy and drugs. MATERIAL AND METHOD A 35-year-old-woman case report is exposed. She has recurrent chylosa ascites, requiring several admissions and evacuatory paracentesis. After food-fat was replaced by medium-chain triacyl-glicerol-enriched diet, a clinical, analytical and anthropometric improvement was demonstrated. CONCLUSIONS The major way of treatment in intestinal lymphangiectasia in this case is the employement of specific-diet and adaptaded-basic-food. It's difficult and high collaboration of the patient is required, being necessary medical revisions during the whole life, due to the not well known evolution of this long-standing disease.

Case Reports; English Abstract; Journal Article;

Identificador

Campos Martín C, Fernández-Argüelles García A, Rabat Restrepo JM, Sendón Pérez A. Dietoterapia en paciente con linfangiectasia intestinal primaria y ascitis quilosa de repetición. Nutr Hosp; 22(6):723-5

1699-5198 (Online)

0212-1611 (Print)

http://hdl.handle.net/10668/760

18051999

Idioma(s)

es

Publicador

Aula Médica Ediciones

Relação

Nutrición hospitalaria : organo oficial de la Sociedad Española de Nutrición Parenteral y Enteral

http://www.nutricionhospitalaria.com/fichadoi.asp?i=3975

Direitos

Acceso abierto

Palavras-Chave #Linfangiectasia #Dietoterapia #MCT #Ascitis quilosa #Lymphangiectasia #Diet-therapy #Chylosa Ascites #Medical Subject Headings::Diseases::Digestive System Diseases::Peritoneal Diseases::Chylous Ascites #Medical Subject Headings::Check Tags::Female #Medical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::Humans #Medical Subject Headings::Diseases::Hemic and Lymphatic Diseases::Lymphatic Diseases::Lymphangiectasis::Lymphangiectasis, Intestinal #Medical Subject Headings::Diseases::Pathological Conditions, Signs and Symptoms::Pathologic Processes::Disease Attributes::Recurrence #Medical Subject Headings::Named Groups::Persons::Age Groups::Adult
Tipo

info:eu-repo/semantics/article

info:eu-repo/semantics/published

Artículo