Oral manifestations of Albright hereditary Osteodystrophy: a case report


Autoria(s): Gomes,Mônica Fernandes; Camargo,Ana Maria Albernaz; Sampaio,Tatiane Alves; Graziozi,Maria Aparecida O. C.; Armond,Mônica Costa
Data(s)

01/08/2002

Resumo

Albright hereditary osteodystrophy is a hereditary metabolic disorder of dominant autosomal etiology that is commonly characterized by short stature, round face, small metacarpus and metatarsus, mental retardation, osteoporosis, subcutaneous calcification, variable hypocalcemia, and hyperphosphatemia. In this study, we report a clinical case of a 17-year-old woman with Albright hereditary osteodystrophy, and we discuss her clinical, radiographic, and laboratory test characteristics together with the oral manifestations, and we correlate them with the characteristics found in the literature. We also discuss the odontological management of treatment of related periodontal disease and planning for corrections of related malocclusions.

Formato

text/html

Identificador

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0041-87812002000400006

Idioma(s)

en

Publicador

Faculdade de Medicina / Universidade de São Paulo - FM/USP

Fonte

Revista do Hospital das Clínicas v.57 n.4 2002

Palavras-Chave #Albright's hereditary osteodystrophy #Pseudohypoparathyroidism #Gs protein #Parathormone #Oral manifestations
Tipo

journal article