Thoracic Duct Decompression for Protein-Losing Enteropathy in Failing Fontan Circulation
Data(s) |
24/05/2016
24/05/2016
01/06/2016
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Resumo |
An infrequent but devastating late complication of Fontan circulation is protein-losing enteropathy (PLE), which results from unbalanced lymphatic homeostasis. Surgical decompression of the thoracic duct by redirecting its drainage to the pulmonary venous atrium has been introduced recently as a possible treatment. This report describes a single-institution experience with this innovative procedure in 2 patients with failing Fontan circulation with PLE refractory to optimized medical therapy. |
Identificador |
Ann Thorac Surg. 2016 Jun;101(6):2370-3 http://hdl.handle.net/10400.17/2507 10.1016/j.athoracsur.2015.08.079 |
Idioma(s) |
eng |
Publicador |
Elsevier |
Direitos |
openAccess |
Palavras-Chave | #HSM CAR PED #HSM ANS #HSM CCT #Adrenal Cortex Hormones/therapeutic use #Atrioventricular Block/etiology #Atrioventricular Block/therapy #Adolescent #Brachiocephalic Veins/diagnostic imaging #Brachiocephalic Veins/surgery #Cardiac Pacing, Artificial #Combined Modality Therapy #Decompression, Surgical/methods #Fontan Procedure/adverse effects #Heart Atria/diagnostic imaging #Heart Atria/surgery #Heart Defects, Congenital/surgery #Hypoplastic Left Heart Syndrome/surgery #Lymphatic System/physiopathology #Norwood Procedures #Protein-Losing Enteropathies/etiology #Protein-Losing Enteropathies/surgery #Pulmonary Veins/surgery #Thoracic Duct/surgery #Tomography, X-Ray Computed #Vasodilator Agents/therapeutic use #Vena Cava, Superior/surgery |
Tipo |
article |