Thoracic Duct Decompression for Protein-Losing Enteropathy in Failing Fontan Circulation


Autoria(s): António, M; Gordo, A; Pereira, C; Pinto, MF; Fragata, I; Fragata, J
Data(s)

24/05/2016

24/05/2016

01/06/2016

Resumo

An infrequent but devastating late complication of Fontan circulation is protein-losing enteropathy (PLE), which results from unbalanced lymphatic homeostasis. Surgical decompression of the thoracic duct by redirecting its drainage to the pulmonary venous atrium has been introduced recently as a possible treatment. This report describes a single-institution experience with this innovative procedure in 2 patients with failing Fontan circulation with PLE refractory to optimized medical therapy.

Identificador

Ann Thorac Surg. 2016 Jun;101(6):2370-3

http://hdl.handle.net/10400.17/2507

10.1016/j.athoracsur.2015.08.079

Idioma(s)

eng

Publicador

Elsevier

Direitos

openAccess

Palavras-Chave #HSM CAR PED #HSM ANS #HSM CCT #Adrenal Cortex Hormones/therapeutic use #Atrioventricular Block/etiology #Atrioventricular Block/therapy #Adolescent #Brachiocephalic Veins/diagnostic imaging #Brachiocephalic Veins/surgery #Cardiac Pacing, Artificial #Combined Modality Therapy #Decompression, Surgical/methods #Fontan Procedure/adverse effects #Heart Atria/diagnostic imaging #Heart Atria/surgery #Heart Defects, Congenital/surgery #Hypoplastic Left Heart Syndrome/surgery #Lymphatic System/physiopathology #Norwood Procedures #Protein-Losing Enteropathies/etiology #Protein-Losing Enteropathies/surgery #Pulmonary Veins/surgery #Thoracic Duct/surgery #Tomography, X-Ray Computed #Vasodilator Agents/therapeutic use #Vena Cava, Superior/surgery
Tipo

article